Pending

Thyroid Hormones in ADPKD
A Study of RGLS8429 in Patients With Autosomal Dominant Polycystic Kidney Disease
Feasibility of Study of Empagliflozin in Patients With Autosomal Dominant Polycystic Kidney Disease
Assessment of Treatment With Laparoscopic Fenestration or Aspiration Sclerotherapy for Large Symptomatic Hepatic Cysts
A GnRH Agonist IN Pre-menopausal Women STudy to Treat Severe Polycystic Liver Disease
Renal Denervation in ADPKD- RDN-ADPKD Study
A Study of RGLS8429 in Healthy Volunteers
Effect of Beetroot Juice on Reducing Hypertension in Autosomal Dominant Polycystic Kidney Disease
HYDROchlorothiazide to PROTECT Polycystic Kidney Disease Patients and Improve Their Quality of Life
Long-Term Treatment and Follow up of Subjects Completing 24 Months of Treatment With Tesevatinib on Study KD019-101
A Trial to Assess the Efficacy and Safety of Octreotide Subcutaneous Depot in Patients With PLD
Open-label, Roll-over Study to Assess Safety of Lixivaptan in Participants With ADPKD Who Completed Study PA-ADPKD-303
Pravastatin and Alkali Therapy in Patients With Autosomal Dominant Polycystic Kidney Disease
A Phase 2 Trial of the Safety and Efficacy of Bardoxolone Methyl in Patients With Rare Chronic Kidney Diseases – PHOENIX
PB to Treat Hereditary Nephrogenic Diabetes Insipidus, ADPKD Treated With Tolvaptan, and Severely Polyuric Patients With Previous Lithium Administration
Tolvaptan Extension Study in Participants With ADPKD
Tolvaptan-Octreotide LAR Combination in ADPKD
Differential Diagnosis and Prognosis of Fetuses with Bilateral Enlarged, Hyperechogenic Kidneys: Renal Volume and Amniotic Fluid Volume with Advancing Gestation
Pre-clinical evaluation of dual targeting of the GPCRs CaSR and V2R as therapeutic strategy for autosomal dominant polycystic kidney disease
Polycystin-1 dependent regulation of polycystin-2 via GRP94, a member of HSP90 family that resides in the endoplasmic reticulum
Genomic analysis of circulating tumor cells in adenosquamous carcinoma of the prostate: a case report
The effect of trichlormethiazide in autosomal dominant polycystic kidney disease patients receiving tolvaptan: a randomized crossover controlled trial
The chloride channel CFTR is not required for cyst growth in an ADPKD mouse model
Inhibiting Focal Adhesion Kinase Ameliorates Cyst Development in Polycystin-1-Deficient Polycystic Kidney Disease in Animal Model
Early-Isolated V Lesion in Kidney Allograft: Acute Rejection or Ischemic Injury? A Case Report of Primary Nonfunction and Graft Loss
Greater adherence to the dietary approaches to stop hypertension dietary pattern is associated with preserved muscle strength in patients with autosomal dominant polycystic kidney disease: a single-center cross-sectional study
Zebrafish Model as a Screen to Prevent Cyst Inflation in Autosomal Dominant Polycystic Kidney Disease
Subclinic arterial and left ventricular systolic impairment in autosomal dominant polycystic kidney disease with preserved renal functions
Agreement of Food Records and 24-Hour Urine Studies in Clinical Practice
Correction to: The wind of change in the management of autosomal dominant polycystic kidney disease in childhood
TAMEing ADPKD with metformin: safe and effective?
Association of autosomal dominant polycystic kidney disease with cerebral small vessel disease
Rapid target validation in a Cas9-inducible hiPSC derived kidney model
Risk Factors for Pain in Autosomal Dominant Polycystic Kidney Disease: A New Research Trajectory
Pain and Obesity in Autosomal Dominant Polycystic Kidney Disease: A Post Hoc Analysis of the Halt Progression of Polycystic Kidney Disease (HALT-PKD) Studies
Metformin Therapy in Autosomal Dominant Polycystic Kidney Disease: A Feasibility Study
The causes and consequences of paediatric kidney disease on adult nephrology care
Tolvaptan in ADPKD Patients With Very Low Kidney Function
Twenty-Year Survival of Kidney Transplant From a Deceased Donor With Autosomal Dominant Polycystic Kidney Disease
Kidney Organoid and Microphysiological Kidney Chip Models to Accelerate Drug Development and Reduce Animal Testing
Case report-Campylobacter jejuni cyst infection in autosomal dominant polycystic kidney disease
The BC ADPKD Network: A Comprehensive Provincial Approach to Support Specialized and Locally Delivered Multidisciplinary ADPKD Care
Short-term changes in micturition patterns with tolvaptan treatment for autosomal dominant polycystic kidney disease
Expanding the variability of the ADPKD-GANAB clinical phenotype in a family of Italian ancestry
Birth of two healthy girls following preimplantation genetic diagnosis and gestational surrogacy in a rapidly progressive autosomal dominant polycystic kidney disease case using tolvaptan
A polycystin-2 protein with modified channel properties leads to an increased diameter of renal tubules and to renal cysts
Symptomatic kidney stones in an anuric patient on dialysis: A case report
Polycystic liver disease with lethal abdominal wall rupture: a case report
Kidney organoids generated from erythroid progenitors cells of patients with autosomal dominant polycystic kidney disease
Possible Role of the Mitochondrial Genome in the Pathogenesis of Autosomal Dominant Polycystic Kidney Disease
Endovascular treatment of intrarenal aneurysms bleeding and angiomyolipomas in a patient with tuberous sclerosis and polycystic kidney disease
Autosomic dominant polycystic kidney disease and metformin: Old knowledge and new insights on retarding progression of chronic kidney disease
The importance of the number of antihypertensives in the progression of autosomal dominant polycystic kidney disease
Polycystin-1 regulates cardiomyocyte mitophagy
Association of Baseline Urinary Metabolic Biomarkers with ADPKD Severity in TAME-PKD Clinical Trial Participants
Extracellular vesicles and exosomes generated from cystic renal epithelial cells promote cyst growth in autosomal dominant polycystic kidney disease
Chronic Inflammation in Chronic Kidney Disease Progression: Role of Nrf2
Identification of pathological transcription in autosomal dominant polycystic kidney disease epithelia
Neonatal polycystic kidney disease: a novel variant
Urinary citrate as a marker of renal function in patients with autosomal dominant polycystic kidney disease
Emerging non-pharmacological interventions in ADPKD: an update on dietary advices for clinical practice
Smoking accelerates renal cystic disease and worsens cardiac phenotype in Pkd1-deficient mice
Identification of novel single-nucleotide variants altering RNA splicing of PKD1 and PKD2
The Effect of Smoking on Endothelial Dysfunction in Autosomal Dominant Polycystic Kidney Disease Patients with Preserved Renal Function
Natural-derived compounds and their mechanisms in potential autosomal dominant polycystic kidney disease (ADPKD) treatment
Ultrabright Plasmonic-Fluor Nanolabel-Enabled Detection of a Urinary ER Stress Biomarker in Autosomal Dominant Tubulointerstitial Kidney Disease
Diagnosis of infected kidney cysts in patients with autosomal dominant polycystic kidney disease and end-stage renal disease
Challenging Disease Ontology by Instances of Atypical PKHD1 and PKD1 Genetics
Pathogenic Variants in the Genes Affected in Alport Syndrome (COL4A3-COL4A5) and Their Association With Other Kidney Conditions: A Review
The vasopressin-aquaporin-2 pathway syndromes
Clinical and genetic characteristics of Korean autosomal dominant polycystic kidney disease patients
Safety Profile of Tolvaptan in the Treatment of Autosomal Dominant Polycystic Kidney Disease
Safety and efficacy of Tolvaptan in real-world patients with autosomal dominant polycystic kidney disease- interim results of SLOW-PKD surveillance
Drug repurposing in autosomal dominant polycystic kidney disease: back to the future with pioglitazone
Founding mutations explains hotspots of polycystic kidney disease in Southern Spain
A randomized phase 1b cross-over study of the safety of low-dose pioglitazone for treatment of autosomal dominant polycystic kidney disease
Autosomal Dominant Polycystic Kidney Disease in which the Polycystic Liver Volume was Reduced by Rigorous Blood Pressure Control
Aquaporin 2 regulation: implications for water balance and polycystic kidney diseases
Gender-Dependent Phenotype in Polycystic Kidney Disease Is Determined by Differential Intracellular Ca(2+) Signals
Coregulation Analysis of Mechanistic Biomarkers in Autosomal Dominant Polycystic Kidney Disease
DEAD-Box RNA Helicases in Cell Cycle Control and Clinical Therapy
Primary prevention of cardiovascular disease events with renin-angiotensin system blockade in autosomal dominant polycystic kidney disease dialysis patients: A nationwide cohort study
Primary results of the randomized trial of metformin administration in polycystic kidney disease (TAME PKD)
Biallelic Mutations in DNAJB11 are Associated with Prenatal Polycystic Kidney Disease in a Turkish Family
The effects of intrinsic apoptosis on cystogenesis in PKD1-deficient ADPKD pig model
PKD1-Associated Arachnoid Cysts in Autosomal Dominant Polycystic Kidney Disease
Blood pressure in children with renal cysts and diabetes syndrome
IMPEDE-PKD Randomised Placebo-controlled Trial
Enhanced MCP-1 Release in Early Autosomal Dominant Polycystic Kidney Disease
Author’s Reply to Correspondence: “Effect of Tolvaptan Treatment on Acid-Base Homeostasis in ADPKD Patients”
Effect of Tolvaptan Treatment on Acid-Base Homeostasis in ADPKD Patients
Biliary peritonitis due to liver cyst rupture in autosomal dominant polycystic kidney disease
Integrative Cistromic and Transcriptomic Analyses Identify CREB Target Genes in Cystic Renal Epithelial Cells
Correction to: “Predictors of progression in autosomal dominant and autosomal recessive polycystic kidney disease”
The cellular pathways and potential therapeutics of Polycystic Kidney Disease
TWEAK Signaling Pathway Blockade Slows Cyst Growth and Disease Progression in Autosomal Dominant Polycystic Kidney Disease
Estrogens in polycystic liver disease: a target for future therapies?
New insights on the role of vascular endothelial growth factor in biliary pathophysiology
Corneal endothelial cell density and microvascular changes of retina and optic disc in autosomal dominant polycystic kidney disease
Pancreas in Hereditary Syndromes: Cross-sectional Imaging Spectrum

Iliac Pseudoaneurysm, Only a Manifestation With More Causes: A Case Report
A case of autosomal dominant polycystic kidney disease with amelioration of refractory cyst infections following prolonged hemodialysis time
Association of autosomal dominant polycystic kidney disease, asymptomatic multiple giant coronary arteries aneurysms and abdominal aortic aneurysm: a case report
Renal and Skeletal Anomalies in a Cohort of Individuals With Clinically Presumed Hereditary Nephropathy Analyzed by Molecular Genetic Testing
A Multitubular Kidney-on-Chip to Decipher Pathophysiological Mechanisms in Renal Cystic Diseases
To Add Weight to Overweight
Overweight and Obesity and Progression of ADPKD
Progression and Regression of Chronic Kidney Disease by Age Among Adults in a Population-Based Cohort in Alberta, Canada
PKD2 gene variants in Chinese patients with autosomal dominant polycystic kidney disease
Effect of tolvaptan in Japanese patients with autosomal dominant polycystic kidney disease: a post hoc analysis of TEMPO 3:4 and TEMPO Extension Japan
The European Rare Kidney Disease Registry (ERKReg): objectives, design and initial results
To Evaluate the Safety, Tolerability, Pharmacokinetics and Pharmacodynamics of Oral AL01211 in Healthy Volunteers and Autosomal Dominant Polycystic Kidney Disease Subjects
Daily Caloric Restriction in ADPKD
Paraneoplastic Polymyositis Due to Renal Cell Carcinoma in a Patient with Autosomal Dominant Polycystic Kidney Disease
Patient-reported outcome measures for pain in autosomal dominant polycystic kidney disease: A systematic review
Fever of Unknown Origin: (18)F-Fluorodeoxyglucose Positron Emission Tomography-Computed Tomography Showing Renal Cyst Infection in Autosomal Dominant Polycystic Kidney Disease
EXPRESS: Preventive screening for intracranial aneurysms
Simultaneous right-sided nephrectomy with orthotopic liver and kidney transplantation-An alternative method for patients with autosomal dominant polycystic liver and kidney disease
Comprehensive strategy improves the genetic diagnosis of different polycystic kidney diseases
A validation study of the kidney failure risk equation in advanced chronic kidney disease according to disease aetiology with evaluation of discrimination, calibration and clinical utility
Reno-appendiceal fistula in autosomal dominant polycystic kidney disease
Aggressive advanced gastric cancer in a patient with autosomal dominant polycystic kidney disease
PKD2 deficiency suppresses amino acid biosynthesis in ADPKD by impairing the PERK-TBL2-eIF2-ATF4 pathway
Fibroblast Growth Factor 23 Is a Valuable Predictor of Autosomal Dominant Polycystic Kidney Disease Progression
Response to “Fibroblast Growth Factor 23 Is a Valuable Predictor of Autosomal Dominant Polycystic Kidney Disease Progression”
Therapeutic advances in ADPKD: the future awaits
Case report: Atypical polycystic kidney disease
Increasing prevalence of hypertension during long-term follow-up in children with autosomal dominant polycystic kidney disease
Cross Talk Between Renal Transporters and Polycystin-1 as a Potential Molecular Target Involved in Autosomal Dominant Polycystic Kidney Disease
Radiographic Imaging in Autosomal Dominant Polycystic Kidney Disease: A Claims Analysis
Congenital hepatic fibrosis: case report and review of literature
The correlation between kidney volume and measured glomerular filtration rate in an Asian ADPKD population: a prospective cohort study
Applications of Herbal Medicine to Treat Autosomal Dominant Polycystic Kidney Disease
Cinacalcet may suppress kidney enlargement in hemodialysis patients with autosomal dominant polycystic kidney disease
Pigmented median raphe cyst of the penis that developed after middle age without infection or trauma history
Short Term Induction of Ketosis in PKD
Regional Variations in Prevalence and Severity of Autosomal Dominant Polycystic Kidney Disease in the United States
Successful endoscopic surgery for emphysematous pyelonephritis in a non-diabetic patient with autosomal dominant polycystic kidney disease: A case report
Spontaneous coronary dissection should not be ignored in patients with chest pain in autosomal dominant polycystic kidney disease: A case report
Inward calcium current through the polycystin-2-dependent channels of renal primary cilia
Nephroplex: a kidney-focused NGS panel highlights the challenges of PKD1 sequencing and identifies a founder BBS4 mutation
Autosomal dominant polycystic kidney disease with liver involvement and left ventricular noncompaction: An unusual coexistence
Molecular genetics of renal ciliopathies
Methionine metabolism: a driver of ADPKD
A comprehensive PGT-M strategy for ADPKD patients with de novo PKD1 mutations using affected embryo or gametes as proband
Factors predicting decline in renal function and kidney volume growth in autosomal dominant polycystic kidney disease: a prospective cohort study (Japanese Polycystic Kidney Disease registry: J-PKD)
Modeling Neoplastic Growth in Renal Cell Carcinoma and Polycystic Kidney Disease
Loss of PKD1 and PKD2 share common effects on intracellular Ca2+ signaling
Prognostic Value of Fibroblast Growth Factor 23 in Autosomal Dominant Polycystic Kidney Disease
Per-Treatment Post Hoc Analysis of Clinical Trial Outcomes With Tolvaptan in ADPKD
Demographic, diagnostic and therapeutic characteristics of autosomal dominant polycystic kidney disease in Ghana
IFT-A deficiency in juvenile mice impairs biliary development and exacerbates ADPKD liver disease
The Effect of Tolvaptan on BP in Polycystic Kidney Disease: A Post Hoc Analysis of the TEMPO 3:4 Trial
Long-term dietary nitrate supplementation does not reduce renal cyst growth in experimental autosomal dominant polycystic kidney disease
Laparoscopic Nephrectomy for Massive Kidneys in Polycystic Kidney Disease
Disconnect in Assessments of Autosomal Dominant Polycystic Kidney Disease Burden Between Patients and Physicians: A Survey Study
Exceptionally Large Kidneys in Autosomal Dominant Polycystic Disease in India
Characterization of Primary Cilia in Osteoblasts Isolated From Patients With ADPKD and CKD
Evaluation of sirtuin 1 (SIRT1) levels in autosomal dominant polycystic kidney disease
Sequential Liver-Kidney Transplantation for Recurrent Liver Cysts Infection in a Patient With Autosomal Dominant Polycystic Kidney Disease: A Case Report
Preventive project of Autosomal Dominant Polycystic Kidney Disease (ADPKD)
Renal Squamous Cell Carcinoma-related Polymyositis in a Patient with Autosomal Dominant Polycystic Kidney Disease
A methionine-Mettl3-N(6)-methyladenosine axis promotes polycystic kidney disease
Phosphorus binders: trigger for intestinal diverticula formation in an ADPKD patient
A Web of Science-based scientometric analysis about mammalian target of rapamycin signaling pathway in kidney disease from 1986 to 2020
The perioperative management of simultaneous bilateral nephrectomy with renal transplantation: a case series
Quinomycin A reduces cyst progression in polycystic kidney disease
Semantic Instance Segmentation of Kidney Cysts in MR Images: A Fully Automated 3D Approach Developed Through Active Learning
Endothelial Dysfunction and Atherosclerosis in Patients With Autosomal Dominant Polycystic Kidney Disease
Effect of Reducing Ataxia-Telangiectasia Mutated (ATM) in Experimental Autosomal Dominant Polycystic Kidney Disease
Predicting liver cyst severity by mutations in patients with autosomal-dominant polycystic kidney disease
Non-Coding RNAs in Hereditary Kidney Disorders
Generation of human induced pluripotent stem cell line (MUi026-A) from a patient with autosomal dominant polycystic kidney disease carrying PKD1 point mutation
Risk of Hospital Encounters With Kidney Stones in Autosomal Dominant Polycystic Kidney Disease: A Cohort Study
Art in the ward: nephrology picture
Aortic Dissection in Familial Patients with Autosomal Dominant Polycystic Kidney Disease
miRNA-16 as a predictive factor for intracranial aneurysms in autosomal dominant polycystic kidney disease
Ciclopirox olamine induces ferritinophagy and reduces cyst burden in polycystic kidney disease
Incident Gallstones During Somatostatin Analog Treatment are Associated with Acute Biliary Complications Especially After Discontinuation
Novel non-cystic features of polycystic kidney disease: having new eyes or seeking new landscapes
Spatiotemporal trends and prognosis of end-stage renal disease patients with biopsy-proven immunoglobulin A nephropathy in France from 2010 to 2014
Glomerular filtration rate is the main predictor of urine volume in autosomal dominant polycystic kidney disease patients treated with tolvaptan when daily osmolar excretion is expressed as urinary osmolality/creatinine ratio
Limitations and opportunities in the pharmacotherapy of ciliopathies
Baseline Characteristics and Patient-Reported Outcomes of ADPKD Patients in the Multicenter TAME-PKD Clinical Trial
Cardiovascular risk factors and the impact on prognosis in patients with chronic kidney disease secondary to autosomal dominant polycystic kidney disease
Metabolic profiling in children and young adults with autosomal dominant polycystic kidney disease
Liver transplantation in adult polycystic liver disease: the Ontario experience
Regulatory Guidelines Do Not Accurately Predict Tolvaptan and Metabolite Interactions at BCRP, OATP1B1 and OAT3 Transporters
B cell and monocyte phenotyping: A quick asset to investigate the immune status in patients with IgA nephropathy
Characteristics of Patients with End-Stage Kidney Disease in ADPKD
Acid-Base Homeostasis During Vasopressin V2 Receptor Antagonist Treatment in Autosomal Dominant Polycystic Kidney Disease Patients
Mechanism and application of metformin in kidney diseases: An update
The underestimated burden of monogenic kidney disease in adults waitlisted for kidney transplantation
Assessing Risk of Rapid Progression in Autosomal Dominant Polycystic Kidney Disease and Special Considerations for Disease-Modifying Therapy
The genetic background significantly impacts the severity of kidney cystic disease in the Pkd1(RC/RC) mouse model of autosomal dominant polycystic kidney disease
Clinical Factors Associated with the Risk of Intracranial Aneurysm Rupture in Autosomal Dominant Polycystic Kidney Disease
A Clinical Trial of Water Therapy for Autosomal Dominant Polycystic Kidney Disease
The wind of change in the management of autosomal dominant polycystic kidney disease in childhood
Comparison of chronic kidney disease trial designs and analysis strategies
Local cAMP signalling cascades – roles and targets in chronic kidney disease?

iPSC technology-based regenerative medicine for kidney diseases
Giant Bilateral Adrenal Myelolipoma: Case Report
Clinical genetic diagnostics in Danish autosomal dominant polycystic kidney disease patients reveal possible founder variants
Diagnostic accuracy of administrative codes for autosomal dominant polycystic kidney disease in clinic patients with cystic kidney disease
Role of the Polycystins as Mechanosensors of Extracellular Stiffness
Corrigendum to “Narita I. Estimating Growth Rate by a Single Measurement of Kidney Volume in ADPKD.” Kidney Int Rep. 2020;5:1383-1384
Patients with Protein-Truncating PKD1 Mutations and Mild ADPKD
Infantile spasms and early-onset progressive polycystic renal lesions associated with TSC2/PKD1 contiguous gene deletion syndrome
A practical guide for the management of acute abdominal pain with fever in patients with autosomal dominant polycystic kidney disease
Potential role of plant miRNAs in the pathogenesis of autosomal dominant polycystic kidney disease: An in silico study
Aquaporins and diseases pathogenesis: From trivial to undeniable involvements, a disease-based point of view
Tolvaptan-induced remission of primary palmar hyperhidrosis in a patient with ADPKD: a serendipitous finding
Polycystic liver disease genes: practical considerations for genetic testing
Adult Inactivation of the Recessive Polycystic Kidney Disease Gene Causes Polycystic Liver Disease
Up-regulation of DNA Damage Response Signaling in Autosomal Dominant Polycystic Kidney Disease
Bilateral Nephrectomy in Patients with Autosomal Dominant Polycystic Kidney Disease and End-Stage Chronic Renal Failure
Prostatic cyst in a pediatric patient with autosomal dominant polycystic kidney disease
Efficacy and Safety of Lixivaptan in the Treatment of Autosomal Dominant Polycystic Kidney Disease
Use of the Urine-to-Plasma Urea Ratio to Predict ADPKD Progression
Cytopenia in autosomal dominant polycystic kidney disease (ADPKD): merely an association or a disease-related feature with prognostic implications?
Using Preimplantation Genetic Diagnosis in Autosomal Dominant Polycystic Kidney Disease Patients: a Multicenter Clinical Trial
Combination of curcumin and ginkgolide B inhibits cystogenesis by regulating multiple signaling pathways
Genitourinary Interventions in Autosomal Dominant Polycystic Kidney Disease: Clinical Recommendations for Urologic and Transplant Surgeons
Renal Lymphangiomatosis Mimicking Polycystic Kidney Disease In An Adult, A Case Report and Literature Review
Utility of Serial Donor-derived Cell-free DNA Measurements for Detecting Allograft Rejection in a Kidney Transplant Recipient After PD-1 Checkpoint Inhibitor Administration
Interferon Regulatory Factor-5 in Resident Macrophage Promotes Polycystic Kidney Disease
Morning blood pressure surge in early autosomal dominant polycystic kidney disease and its relation with left ventricular hypertrophy
Assessment of Renal Volume with MRI: Experimental Protocol
Predictors of progression in autosomal dominant and autosomal recessive polycystic kidney disease
Preservation of kidney function irrelevant of total kidney volume growth rate with tolvaptan treatment in patients with autosomal dominant polycystic kidney disease
Excess Healthcare Costs in Patients with Autosomal Dominant Polycystic Kidney Disease by Renal Dysfunction Stage
Turner syndrome and autosomal dominant polycystic kidney disease
Bilateral Laparoscopic Nephrectomy in Autosomal Dominant Polycystic Kidney Disease with Bilateral Renal Masses: A Feasible Option
The genetic landscape of polycystic kidney disease in Ireland
Use of Low Dose Pioglitazone to Treat Autosomal Dominant Polycystic Kidney Disease
Renal transplant outcomes in amyloidosis
Genomic diagnostics in polycystic kidney disease: an assessment of real-world use of whole-genome sequencing
Analysis of mutations in six Chinese families with autosomal dominant polycystic kidney disease
Ehlers-Danlos Syndrome: Immunologic contrasts and connective tissue comparisons
Long-term Treatment of Autosomal Dominant Polycystic Kidney Disease (ADPKD) With Venglustat
Cardiovascular disorders in autosomal dominant polycystic kidney disease
Prevalence of Inferior Vena Cava Compression in ADPKD
Analysis of PKD2 gene variant and protein localization in a pedigree affected with polycystic kidney disease
Genetic and Sporadic Renal Cystic Diseases During the Perinatal and Neonatal Period: Core Curriculum 2021
Liver Infarction and Venous Thromboembolism after Tamoxifen Use in an ADPKD Patient with Encapsulating Peritoneal Sclerosis: A Case Report
Suppression of Foxo3-Gatm by miR-132-3p Accelerates Cyst Formation by Up-Regulating ROS in Autosomal Dominant Polycystic Kidney Disease
Renal Denervation for Resistant Hypertension: Time to Improve Patient Selection. The Lesson From ADPKD
Dickkopf-3: Current Knowledge in Kidney Diseases
Serum uromodulin levels, MR imaging findings, and their relationship with eGFR-based CKD staging in ADPKD patients
Renal Cyst
Pancreas Imaging
Simultaneous laparoscopic bilateral nephrectomy as a preparation for kidney transplantation in patients with autosomal dominant polycystic kidney disease
Multicenter Study of Long-Term Safety of Tolvaptan in Later-Stage Autosomal Dominant Polycystic Kidney Disease
Long-Term Safety of Tolvaptan in ADPKD: Where Do We Stand?
Serum bicarbonate is associated with kidney outcomes in autosomal dominant polycystic kidney disease
Clinical and Molecular Description of PKD1 and PKD2 Mutation Negative Carriers in ADPKD
Deep Learning Assisted Localization of Polycystic Kidney on Contrast-Enhanced CT Images
Study of the Efficacy and Safety of Tesevatinib in Subjects With ADPKD
Ketogenic Dietary Interventions in Autosomal Dominant Polycystic Kidney Disease (ADPKD)
A Comparison of Urine Dilution Ability between Adult Dominant Polycystic Kidney Disease, Other Chronic Kidney Diseases, and Healthy Control Subjects: A Case-Control Study
Exploring the Spectrum of Kidney Ciliopathies
ETIOLOGIES AND OUTCOMES OF PRENATALLY DIAGNOSED HYPERECHOGENIC KIDNEYS
Time Restricted Feeding in Autosomal Dominant Polycystic Kidney Disease
Autosomal dominant polycystic kidney disease : a pediatric perspective
MicroRNAs and Polycystic Kidney Disease
Autosomal dominant polycystic kidney disease and pioglitazone for its therapy: a comprehensive review with an emphasis on the molecular pathogenesis and pharmacological aspects
Effect of Statins on Renal Function and Total Kidney Volume in Autosomal Dominant Polycystic Kidney Disease
DEMOGRAPHIC AND CLINICAL CHARACTERISTICS OF CHILDREN WITH AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE: A SINGLE CENTER EXPERIENCE
Variable Expressivity of HNF1B Nephropathy, From Renal Cysts and Diabetes to Medullary Sponge Kidney Through Tubulo-interstitial Kidney Disease
Interactions between FGF23 and Genotype in Autosomal Dominant Polycystic Kidney Disease
Curcumin therapy to treat vascular dysfunction in children and young adults with autosomal dominant polycystic kidney disease: Design and baseline characteristics of participants
Suspected Pulmonary Embolism Postcesarean Section in a Patient with Autosomal Dominant Polycystic Kidney Disease
Complications in Patients With Autosomal Dominant Polycystic Kidney Disease Undergoing Ureteroscopy: A Cohort Study
Clinical and genetic spectra of kidney disease caused by REN mutations
Percutaneous nephrolithotomy under X ray free technique in upper urinary stone patients with autosomal dominant polycystic kidney disease: experience from a large-volume stone management center
Autosomal Dominant Polycystic Kidney Disease does not significantly alter major COVID-19 outcomes among veterans
The Controversial Role of Fibrosis in Autosomal Dominant Polycystic Kidney Disease
Semi-Mechanistic Pharmacokinetic Model to Guide the Dose Selection of Nimotuzumab in Patients with Autosomal Dominant Polycystic Kidney Disease
The ELiSA Study – Evaluation of Lixivaptan in Subjects With Autosomal Dominant Polycystic Kidney Disease
Endoplasmic Reticulum Calcium Homeostasis in Kidney Disease: Pathogenesis and Therapeutic Targets
Cyst Reduction by Melatonin in a Novel Drosophila Model of Polycystic Kidney Disease
Overexpression of DJ-1 alleviates autosomal dominant polycystic kidney disease by regulating cell proliferation, apoptosis, and mitochondrial metabolism in vitro and in vivo
Imaging Identification of Rapidly Progressing Autosomal Dominant Polycystic Kidney Disease: Simple Eligibility Criterion for Tolvaptan
Giant Cavernous Hemangioma of the Liver in a Patient with Autosomal Dominant Polycystic Kidney Disease
Serum Copeptin, NLPR3, and suPAR Levels among Patients with Autosomal-Dominant Polycystic Kidney Disease with and without Impaired Renal Function
Disrupting Polycystin-2 EF hand Ca(2+) affinity does not alter channel function or contribute to polycystic kidney disease
Methylation of the PKD1 Promoter Inversely Correlates with its Expression in Autosomal Dominant Polycystic Kidney Disease
Biallelic inheritance of hypomorphic PKD1 variants is highly prevalent in very early onset polycystic kidney disease
Pathogenesis of Congenital Malformations: Possible Role of Oxidative Stress
Urinary CD80 Discriminates Among Glomerular Disease Types and Reflects Disease Activity
The heteromeric PC-1/PC-2 polycystin complex is activated by the PC-1 N-terminus
Overexpression of TGF-beta1 induces renal fibrosis and accelerates the decline in kidney function in polycystic kidney disease
Safety, Pharmacokinetics, Tolerability and Efficacy of Tolvaptan in Children and Adolescents With ADPKD (Autosomal Dominant Polycystic Kidney Disease)
Neonatal Polycystic Kidney Disease in a One-Day-Old Baby: A Case Report
Wishing to Decrease Aquaresis in ADPKD Patients Treated With a V2Ra; the Effect of Regulating Protein and Salt
Thiazide diuretics and the rate of disease progression in autosomal dominant polycystic kidney disease: an observational study
Assessment of Dietary Sodium Intake Using the Scored Salt Questionnaire in Autosomal Dominant Polycystic Kidney Disease
Clinical characteristics associated with 1-year tolvaptan efficacy in autosomal dominant polycystic kidney disease with a wide range of kidney functions
Effect of Vasopressin on the Hypothalamic-Pituitary-Adrenal Axis in ADPKD Patients during V2 Receptor Antagonism
Epidemiology of autosomal-dominant polycystic liver disease in Olmsted county

Renal epithelial and stromal tumor with a multiple cystic lesion localized in the upper portion of the right kidney
Effect of tolvaptan on renal involvement in patients with autosomal dominant polycystic kidney disease according to different gene mutations
An Extended Access Program for Bardoxolone Methyl in Patients With CKD (EAGLE)
Expert-level segmentation using deep learning for volumetry of polycystic kidney and liver
Ivemark II syndrome, a renal-hepatic-pancreatic dysplasia
Interventional Approaches for Loin Pain Hematuria Syndrome and Kidney-Related Pain Syndromes
Cross-talk between CDK4/6 and SMYD2 regulates gene transcription, tubulin methylation, and ciliogenesis
Prevalence, risk factors and disease knowledge of polycystic kidney disease in Pakistan
Autosomal Dominant Polycystic Kidney Disease
Implicating the effect of ketogenic diet as a preventive measure to obesity and diabetes mellitus
TAZ/Wnt-beta-catenin/c-MYC axis regulates cystogenesis in polycystic kidney disease
A Safety, Pharmacokinetic and Dose-Escalation Study of KD019 (Tesevatinib) in Subjects With ADPKD
Proceedings From a Canadian Nephrology Forum: Nephrology Is Back
A novel monogenic preimplantation genetic testing strategy for sporadic polycystic kidney caused by de novo PKD1 mutation
Recognition and Management of a Less Common Cause of Chronic Kidney Disease: Autosomal Dominant Polycystic Kidney Disease
Novel GANAB variants associated with polycystic liver disease
Recognizing and treating autosomal dominant polycystic kidney disease
Feasibility Study of Metformin Therapy in ADPKD
Daily Caloric Restriction and Intermittent Fasting in Overweight and Obese Adults With Autosomal Dominant Polycystic Kidney Disease
Tolvaptan- and Tolvaptan-Metabolite-Responsive T Cells in Patients with Drug-Induced Liver Injury
Characteristics and Outcomes of Kidney Transplant Recipients Requiring High-Acuity Care After Transplant Surgery: A 10-Year Single-Center Study
Shedding light on drug-induced liver injury: activation of T-cells from drug naive human donors with tolvaptan and a hydroxybutyric acid metabolite
Generation of induced pluripotent stem cell PLAFMCi002-A derived from peripheral blood mononuclear cells of polycystic kidney disease patient with PKD1 mutation
Sarcomatoid renal cell carcinoma with autosomal dominant polycystic kidney disease: a case report and literature review
Intracranial aneurysms in renal transplant recipients with autosomal dominant polycystic kidney disease
Cyclin-Dependent Kinase 1 Activity Is a Driver of Cyst Growth in Polycystic Kidney Disease
‘A sword of Damocles’: patient and caregiver beliefs, attitudes and perspectives on presymptomatic testing for autosomal dominant polycystic kidney disease: a focus group study
Safety and Tolerability of Tolvaptan in an Autosomal Dominant Polycystic Kidney Disease Spanish Cohort: A Real-World Experience
African American polycystic kidney patients receive higher risk kidneys, but do not face increased risk for graft failure or post-transplant mortality
A Trial of Bardoxolone Methyl in Patients With ADPKD – FALCON
A Study to Evaluate the Effects of GLPG2737 in Participants With Autosomal Dominant Polycystic Kidney Disease (ADPKD)
A Medical Research Study Designed to Determine if Venglustat Can be a Future Treatment for ADPKD Patients
Renal cystic diseases during the perinatal and neonatal period
Quetiapine-induced thrombotic microangiopathy in a patient on maintenance dialysis
SNX9 Inhibits Cell Proliferation and Cyst Development in Autosomal Dominant Polycystic Kidney Disease via Activation of the Hippo-YAP Signaling Pathway
Disease causing property analyzation of variants in 12 Chinese families with polycystic kidney disease
Loss of PKD1/polycystin-1 impairs lysosomal activity in a CAPN (calpain)-dependent manner
Hemorrhagic Cysts and Other MR Biomarkers for Predicting Renal Dysfunction Progression in Autosomal Dominant Polycystic Kidney Disease
Safety of Lixivaptan in Subjects Previously Treated With Tolvaptan for Autosomal Dominant Polycystic Kidney Disease
Quality of Life in Autosomal Dominant Polycystic Kidney Disease Patients Treated With Tolvaptan
Cardiovascular risk and quality of life in autosomal dominant polycystic kidney disease patients in therapy with tolvaptan: A pilot study
Type IV choledochal cyst with polycystic kidney disease: a case report
Identification of missense and synonymous variants in Iranian patients suffering from autosomal dominant polycystic kidney disease
A Provincial Survey of the Contemporary Management of Autosomal Dominant Polycystic Kidney Disease
Estimation of Changes in Kidney Volume Growth Rate in ADPKD
Estimating Growth Rate by a Single Measurement of Kidney Volume in ADPKD
Hypertension Management in Patients With Autosomal Dominant Polycystic Kidney Disease: Time for a Paradigm Shift?
The importance of the number of antihypertensives in the progression of autosomal dominant polycystic kidney disease
Autophagy induction promotes renal cyst growth in polycystic kidney disease
Markers of endothelial dysfunction and arterial stiffness in patients with early-stage autosomal dominant polycystic kidney disease: a meta-analysis
Automatic semantic segmentation of kidney cysts in MR images of patients affected by autosomal-dominant polycystic kidney disease
Simultaneous bilateral laparoscopic nephrectomy with kidney transplantation in patients with ESRD due to ADPKD: A single-center experience
Mineral bone disease in autosomal dominant polycystic kidney disease
Association between urinary biomarkers and disease progression in adults with autosomal dominant polycystic kidney disease
Tolvaptan-Octreotide LAR Combination in ADPKD
Application of immunosuppressants in patients with autosomal dominant polycystic kidney disease after kidney transplantation
Delayed thromboembolic events after coiling of unruptured intracranial aneurysms in a prospective cohort of 335 patients
A Study of RGLS4326 in Patients With Autosomal Dominant Polycystic Kidney Disease
Sudden Unexpected Death of Infantile Dilated Cardiomyopathy with JPH2 and PKD1 Gene Variants
A Safety, Pharmacokinetic and Dose-Escalation Study of KD019 (Tesevatinib) in Subjects With ADPKD
Safety of Lixivaptan in Subjects Previously Treated With Tolvaptan for Autosomal Dominant Polycystic Kidney Disease
Tolvaptan
Colonic diverticular disease in autosomal dominant polycystic kidney disease: is there really an association? A nationwide analysis
A Clinical Trial of Water Therapy for Autosomal Dominant Polycystic Kidney Disease
Time Restricted Feeding in Autosomal Dominant Polycystic Kidney Disease
Urine concentration ability is reduced to the same degree in adult dominant polycystic kidney disease compared with other chronic kidney diseases in the same CKD-stage and lower THAN in healthy control subjects – a CASE control study
The effect of trehalose on autophagy-related proteins and cyst growth in a hypomorphic Pkd1 mouse model of autosomal dominant polycystic kidney disease
The ELiSA Study – Evaluation of Lixivaptan in Subjects With Autosomal Dominant Polycystic Kidney Disease
Simultaneous hand-assisted laparoscopic bilateral native nephrectomy and kidney transplantation for patients with large polycystic kidneys
Prognostic significance of the albumin-to-globulin ratio for upper tract urothelial carcinoma
Cyst growth in ADPKD is prevented by pharmacological and genetic inhibition of TMEM16A in vivo
Preimplantation Genetic Testing for Monogenic Kidney Disease
Metabolic Changes in Polycystic Kidney Disease as a Potential Target for Systemic Treatment
Pharmacokinetics, Pharmacodynamics, Safety, and Tolerability of Oral Venglustat in Healthy Volunteers
Pansomatostatin Agonist Pasireotide Long-Acting Release for Patients with Autosomal Dominant Polycystic Kidney or Liver Disease with Severe Liver Involvement: A Randomized Clinical Trial
An Extended Access Program for Bardoxolone Methyl in Patients With CKD (EAGLE)
A Trial of Bardoxolone Methyl in Patients With ADPKD – FALCON
Management of Large Allograft Mass Following Living Donor Kidney Transplantation
Tolvaptan or transplant: why wait?